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ERGIC53 Monoclonal Antibody
ERGIC53 Monoclonal Antibody
- 中文名称:
- ERGIC53 Monoclonal Antibody
- 英文名称:
- ERGIC53 Monoclonal Antibody
- 品牌:
- AAA Biotech
- 品牌介绍:
- AAA Biotech专注于为全球生命科学研究提供高品质的蛋白质研究工具,核心产品包括经严格验证的抗体、重组蛋白及ELISA试剂盒。
- 货号:
- AAA41014
- 规格:
- 0.1 mg|2x0.1 mg|3x0.1 mg|4x0.1 mg|5x0.1 mg
- 保存建议:
- ERGIC53 Monoclonal antibody can be stored at 4˚C for three months and -20˚C, stable for up to one year.
- 货期:
- 6-8周
- 来源宿主:
- Mouse
- 反应种属:
- Human, mouse
- 应用:
- ICC (Immunocytochemistry), WB (Western Blot), ELISA
- 免责声明:
- *本产品仅供科研实验使用,不得用于临床诊断。*
- 其他:
克隆性:Monoclonal
同型:IgG1
克隆号:N/A
特异性:At least two isoforms of ERGIC53 are known to exist.
纯度:ERGIC53 Monoclonal Antibody is Protein A purified.
形式:Liquid
浓度:1 mg/mL
- 说明书:
ERGIC53 Monoclonal Antibody: ERGIC53, also known as lectin mannose-binding 1 (LMAN1) protein is a type I integral membrane protein localized in the intermediate region between the endoplasmic reticulum and the Golgi, presumably recycling between the two compartments. The protein is a mannose-specific lectin and is a member of a novel family of plant lectin homologs in the secretory pathway of animal cells. Mutations in the gene are associated with a coagulation defect. Using positional cloning, the gene was identified as the disease gene leading to combined factor V-factor VIII deficiency, a rare, autosomal recessive disorder in which both coagulation factors V and VIII are diminished.